Primary pulmonary hypertension (PPH) is a rare disease. It is high blood pressure in the blood vessels of the lungs.

A person with PPH has extra muscle in the walls of these blood vessels. That extra muscle makes it more difficult for blood to flow through them. As a result, the right side of the heart has to work harder to push blood to the lungs. This additional strain can eventually lead to heart failure.

PPH is a serious condition. It requires care from your doctor.

Heart and Lungs
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The cause of PPH is unknown. Several factors may contribute to the development of the disease, including:

  • Immune system disease
  • Exposure to certain drugs or chemicals
  • Genetic defects